قالب:انزيمات أيض الأحماض الأمينية

أيض: أيض الأحماض الأمينية - synthesis and catabolism enzymes (essential in CAPS)

LYSINE→	Saccharopine dehydrogenase - Glutaryl-CoA dehydrogenase
LEUCINE→	Branched chain aminotransferase - Branched-chain alpha-keto acid dehydrogenase complex - Isovaleryl coenzyme A dehydrogenase - Methylcrotonyl-CoA carboxylase - Methylglutaconyl-CoA hydratase - 3-hydroxy-3-methylglutaryl-CoA lyase
TRYPTOPHAN→	Indoleamine 2,3-dioxygenase/Tryptophan 2,3-dioxygenase - Arylformamidase - Kynureninase - 3-hydroxyanthranilate oxidase - Aminocarboxymuconate-semialdehyde decarboxylase - Aminomuconate-semialdehyde dehydrogenase
PHENYLALANINE→tyrosine→	(see below)

glycine→serine→	Serine hydroxymethyltransferase - Serine dehydratase
alanine→	Alanine transaminase
cysteine→	D-cysteine desulfhydrase
threonine→	L-threonine dehydrogenase

HISTIDINE→	Histidine ammonia-lyase - Urocanate hydratase - Formiminotransferase cyclodeaminase
proline→	Proline oxidase - Pyrroline-5-carboxylate reductase - 1-Pyrroline-5-carboxylate dehydrogenase/ALDH4A1 - PYCR1
arginine→	Ornithine aminotransferase - Ornithine decarboxylase - Agmatinase
→alpha-ketoglutarate→TCA	Glutamate dehydrogenase

G→propionyl-CoA

VALINE→	Branched chain aminotransferase - Branched-chain alpha-keto acid dehydrogenase complex - Enoyl-CoA hydratase - 3-hydroxyisobutyryl-CoA hydrolase - 3-hydroxyisobutyrate dehydrogenase - Methylmalonate semialdehyde dehydrogenase
ISOLEUCINE→	Branched chain aminotransferase - Branched-chain alpha-keto acid dehydrogenase complex - 3-hydroxy-2-methylbutyryl-CoA dehydrogenase
METHIONINE→	Methionine adenosyltransferase - Adenosylhomocysteinase - Cystathionine beta synthase - Cystathionine gamma-lyase (methionine synthesis: MTR/Homocysteine methyltransferase)
THREONINE→	Threonine aldolase
→succinyl-CoA→TCA	Propionyl-CoA carboxylase - Methylmalonyl CoA epimerase - Methylmalonyl-CoA mutase

PHENYLALANINE→tyrosine→	Phenylalanine hydroxylase - Tyrosine aminotransferase - 4-Hydroxyphenylpyruvate dioxygenase - Homogentisate 1,2-dioxygenase - Fumarylacetoacetate hydrolase

G→oxaloacetate

asparagine→aspartate→	Asparaginase/Asparagine synthetase - Aspartate transaminase

Other

tyrosine→melanin	Tyrosinase
cysteine+glutamate→glutathione	Gamma-glutamylcysteine synthetase - Glutathione synthetase - Gamma-glutamyl transpeptidase
glycine→creatine	Guanidinoacetate N-methyltransferase - Creatine kinase
glutamate→glutamine	Glutamine synthetase - Glutaminase
proline+lysine→كولاجين	Prolyl hydroxylase - Lysyl hydroxylase

see also disorders, intermediates

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